T E XTB O
OK P
ICT U R
E
MEDICAL DIAGNOSIS CLINICAL SIGNS/SYMPTOMS MEDICAL MANAGEMENT
NAM E
:
Cystic Fibrosis
DES C RI P
T IO N
:
Cystic fibrosis (CF) is an autosomal recessive,
multisystem disease characterized by altered
transport of sodium and chloride ions in and
out of epithelial cells. This defect primarily
affects the lungs, GI tract (pancreas and
biliary tract), and reproductive tract.
ā
SI G NS/ S
Y M P
T O M
S :
ā¢Meconium ileus in newborn (20%)
ā¢Abdominal Distention
ā¢Vomiting
ā¢MalnutritionāRAPID Dehydration
ā¢No stools
COMPLI C
A T IO N
S
:
Osteoporosis
sinus,
liver disease.
digital clubbing occurs.
Respiratory failure
Pneumothorax
hemoptysis
MEDIC A L MAN A
G EMENT :
antibiotics to prevent and treat chest
infections
Mucolytics to thin mucus in the lungs and
make it easier to cough up
Bronchodilators to widen the airways and
reduce inflammation
Anti-inflammatory agents
CFTR potentiators and correctors
S U R
G ICAL M
ANA G EMEN T
:
NURSING MANAGEMENT
Concept
Impaired airway clearance
Concept
Impaired respiratory system function
Concept
Impaired nutritional status
N U RSING IN T E R
VEN T IO NS
: N U RSING IN T E R
VEN T IO NS
: N U RSING IN T E R
VEN T IO NS
:
1. chest physiotherapy to lossen secretions
and
1. add humified O2 to increase 1. increase sodium intake in food to
replenish sodium that is lost
2. Cough & deep breathe 2. decrease temperature in room to prevent
diaphoresis and sodium loss.
2.add pancreatic enzymes to each meals to
help with nutritional status and absorption
of fat soluble vitamins
3. clear drainage by postural tripoding
3. Position patient accordingly to mobilize
secretions. If secretions are in the upper lobes,
supine positioning is optimal. If in the middle or
lower lobes, upright is best. If in the right or left
lungs, the patient should lay on that side.
3. Offer meal with normal diet with
additional energy and unrestricted fat intake
is recommended
REFERENCE(S)
Kwong, M.H.D.R.C.R.D.H. J. (2018).īLewis's Medical-Surgical Nursingī(11th ed.). Elsevier Health
Sciences (US).īhttps://pageburstls.elsevier.com/books/9780323551496.
